Multicentric reticulohistiocytosis in a Taiwanese woman with Sjögren syndrome

Lan hsin Cheng, Ying Yi Chiang

研究成果: 雜誌貢獻文章同行評審

1 引文 斯高帕斯(Scopus)

摘要

Multicentric reticulohistiocytosis is a rare, non-Langerhans cell histiocytosis characterized by specific skin lesions and destructive arthritis. Clinically, it generally presents with multiple reddish-brown papulonodules over the hands, face, and trunk. The associated destructive arthropathy tends to be severe, with 50% of patients developing arthritis mutilans. Approximately 25-30% of patients present with neoplasia. Coexisting autoimmune diseases are also commonly reported. Here we report the case of a 59-year-old Taiwanese woman with underlying Sjögren syndrome who presented with the typical skin manifestations of multicentric reticulohistiocytosis and early interphalangeal joint involvement. The patient later showed partial response to methotrexate treatment.

原文英語
頁(從 - 到)42-45
期刊Dermatologica Sinica
34
發行號1
DOIs
出版狀態已發佈 - 三月 1 2016

ASJC Scopus subject areas

  • 皮膚科

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