Giant intracranial mesenchymal chondrosarcoma with uncal herniation

Hung Shih Lin, Cheng Chia Tsai, Cheng Kuei Chang, Shiu Jau Chen

研究成果: 雜誌貢獻文章

3 引文 (Scopus)

摘要

Mesenchymal chondrosarcomas are very rare central nervous system (CNS) tumors consisting of undifferentiated mesenchymal cells plus islets of cartilage. We report a case of giant intracranial mesenchymal chondrosarcomas presenting with acute neurologic deterioration. A 22-year-old woman presented with right facial and hand numbness and ocular torsion for about 2 weeks. Magnetic resonance imaging (MRI) disclosed a mass in the right middle cranial fossa with a mass effect. Two days before scheduled surgery, the patient suddenly lost consciousness and was found to have uncal herniation. At emergency surgery, the tumor was totally excised. Pathologically, there was a dimorphic pattern of undifferentiated cells and islets of cartilage, consistent with mesenchymal chondrosarcoma. Although the patient survived surgery, she remained in a vegetative state. The tumor recurred 3 years after surgery. Intracranial mesenchymal chondrosarcoma is rare and should be considered when evaluating a tumor with dural involvement, particularly in younger adults. Differential diagnoses include intracranial meningioma and schwannoma. An aggressive surgical resection is highly recommended because of the high risk of recurrence.
原文英語
頁(從 - 到)93-96
頁數4
期刊Formosan Journal of Surgery
45
發行號3
DOIs
出版狀態已發佈 - 六月 2012

指紋

Mesenchymal Chondrosarcoma
Islets of Langerhans
Cartilage
Middle Cranial Fossa
Persistent Vegetative State
Central Nervous System Neoplasms
Neoplasms
Hypesthesia
Neurilemmoma
Meningioma
Consciousness
Nervous System
Young Adult
Emergencies
Differential Diagnosis
Hand
Magnetic Resonance Imaging
Recurrence

ASJC Scopus subject areas

  • Surgery

引用此文

Giant intracranial mesenchymal chondrosarcoma with uncal herniation. / Lin, Hung Shih; Tsai, Cheng Chia; Chang, Cheng Kuei; Chen, Shiu Jau.

於: Formosan Journal of Surgery, 卷 45, 編號 3, 06.2012, p. 93-96.

研究成果: 雜誌貢獻文章

Lin, Hung Shih ; Tsai, Cheng Chia ; Chang, Cheng Kuei ; Chen, Shiu Jau. / Giant intracranial mesenchymal chondrosarcoma with uncal herniation. 於: Formosan Journal of Surgery. 2012 ; 卷 45, 編號 3. 頁 93-96.
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