Dural sinus hypertension due to segmental stenosis

We report a rare case with dural sinus hypertension due to segmental stenosis, associated with leptomeningeal angiomatosis and drainage from the diploic veins. The etiology and natural history still remain unknown. To differentiate dural sinus stenosis from the sinus thrombosis, the computed tomography venography appears to be a better tool than the other vascular imaging studies including the digital subtraction angiography in such a case. Dural sinus stenosis should be a differential diagnosis for patients with clinical presentations of intracranial hypertension with or without focal neurological deficits.