Clinical spectrum and long-term outcome of ebstein's anomaly based on a 26-year experience in an asian cohort

Ya Mei Chang, Jou Kou Wang, Sheunn Nan Chiu, Ming Tai Lin, En Ting Wu, Chun An Chen, Shu Chien Huang, Yih Sharng Chen, Chung I. Chang, Ing Sh Chiu, Jiunn Lee Lin, Ling Ping Lai, Mei Hwan Wu

研究成果: 雜誌貢獻文章

17 引文 斯高帕斯(Scopus)

摘要

Ebstein's anomaly is a rare, congenital cardiac anomaly that may result in cyanosis, right heart failure, and tachyarrhythmia during the newborn stage or after adolescence. This study investigated the data of 77 patients diagnosed between 1980 and 2006 at a tertiary care center in Taiwan. Patients were grouped into either an early group or a late group. Survival declined rapidly within the newborn stage in the early group, but declined only during the third decade in the late group. Surgical results were poor (20% success rate) for neonatal systemic-to-pulmonary shunts in those cases with associated pulmonary atresia, but were satisfactory for other surgical modes. Supraventricular tachyarrhythmia occurred in 31 (41%) patients at a median age of 10 years and could be eliminated by radiofrequency ablation (81% success rate), though the recurrence rate was high (41%). In conclusion, other than those cases requiring shunts at the newborn stage, the long-term outcome was favorable.
原文英語
頁(從 - 到)685-690
頁數6
期刊European Journal of Pediatrics
168
發行號6
DOIs
出版狀態已發佈 - 六月 1 2009
對外發佈Yes

    指紋

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

引用此

Chang, Y. M., Wang, J. K., Chiu, S. N., Lin, M. T., Wu, E. T., Chen, C. A., Huang, S. C., Chen, Y. S., Chang, C. I., Chiu, I. S., Lin, J. L., Lai, L. P., & Wu, M. H. (2009). Clinical spectrum and long-term outcome of ebstein's anomaly based on a 26-year experience in an asian cohort. European Journal of Pediatrics, 168(6), 685-690. https://doi.org/10.1007/s00431-008-0820-0