Acute life-threatening arrhythmias caused by severe hyperkalemia after induction of anesthesia in an infant with methylmalonic acidemia

Pei Wen Chao, Wen Kuei Chang, Wen I. Lai, Chinsu Liu, Kwok Hon Chan, Cheng Ming Tsao

研究成果: 雜誌貢獻文章

9 引文 (Scopus)

摘要

Methylmalonic acidemia (MMA) is a very rare genetic disease of metabolism that progressively leads to neurological and renal sequelae. This report describes an unusual case of a patient with MMA who developed severe hyperkalemia and severe dysrhythmia during anesthesia. A 13-month-old male infant with MMA underwent urgent insertion of a port-a-cath under general anesthesia. A life-threatening arrhythmia suddenly occurred, with severe hyperkalemia (up to 7.4 mmol/L), immediately following induction of anesthesia. Emergent resuscitation was successfully carried out, with a complete neurological recovery after 7 days after surgery. Although MMA is a rare complication, the possibility of severe hyperkalemia should be considered in the differential diagnosis of patients with MMA presenting with wide QRS complex tachycardia. The management and intraoperative complications of this disorder are reported here, and the available literature is reviewed.
原文英語
頁(從 - 到)243-245
頁數3
期刊Journal of the Chinese Medical Association
75
發行號5
DOIs
出版狀態已發佈 - 五月 1 2012
對外發佈Yes

指紋

Hyperkalemia
Cardiac Arrhythmias
Anesthesia
Inborn Genetic Diseases
Intraoperative Complications
Rare Diseases
Ambulatory Surgical Procedures
Tachycardia
Resuscitation
General Anesthesia
Differential Diagnosis
Methylmalonic acidemia
Kidney

ASJC Scopus subject areas

  • Medicine(all)

引用此文

Acute life-threatening arrhythmias caused by severe hyperkalemia after induction of anesthesia in an infant with methylmalonic acidemia. / Chao, Pei Wen; Chang, Wen Kuei; Lai, Wen I.; Liu, Chinsu; Chan, Kwok Hon; Tsao, Cheng Ming.

於: Journal of the Chinese Medical Association, 卷 75, 編號 5, 01.05.2012, p. 243-245.

研究成果: 雜誌貢獻文章

Chao, Pei Wen ; Chang, Wen Kuei ; Lai, Wen I. ; Liu, Chinsu ; Chan, Kwok Hon ; Tsao, Cheng Ming. / Acute life-threatening arrhythmias caused by severe hyperkalemia after induction of anesthesia in an infant with methylmalonic acidemia. 於: Journal of the Chinese Medical Association. 2012 ; 卷 75, 編號 5. 頁 243-245.
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AU - Tsao, Cheng Ming

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