Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein's anomaly

C. J. Huang, I. S. Chiu, F. Y. Lin, W. J. Chen, J. L. Lin, H. M. Lo, M. H. Wu, S. H. Chu

Research output: Contribution to journalArticle

36 Citations (Scopus)

Abstract

Background: Repairing Ebstein's anomaly without correction of associated arrhythmia may result in sudden death. Catheter or surgical ablation is indicated for various symptomatic tachyarrhythmias in Ebstein's anomaly. Methods: Between October 1973 and October 1997, 30 patients with Ebstein's anomaly underwent surgical repair in our hospital. Tricuspid valve replacement was performed in 13 patients, tricuspid annuloplasty and valvuloplasty in the remaining 17 patients. Preoperative electrophysiological studies were performed in 11 patients after 1980. Concomitant arrhythmia ablation was done in 10 patients: 4 for Wolff-Parkinson-White syndrome, 2 for atrioventricular (AV) nodal reentrant tachycardia, one for ventricular tachycardia and 3 for paroxysmal atrial flutter and fibrillation. Results: No mortality or major morbidity occurred in those patients undergoing arrhythmia intervention. There were 7 deaths in total; 6 died suddenly, and the other died of purulent mediastinitis. None of the 6 sudden deaths underwent preoperative electrophysiological evaluation. The functional recovery was good in all survivals. Conclusions: We conclude that detailed preoperative electrophysiological evaluation in patients with Ebstein's anomaly is mandatory. Aggressive surgical intervention of the associated arrhythmias in addition to anatomic correction can reduce the sudden death in Ebstein's anomaly.

Original languageEnglish
Pages (from-to)347-350
Number of pages4
JournalThoracic and Cardiovascular Surgeon
Volume48
Issue number6
DOIs
Publication statusPublished - Dec 1 2000
Externally publishedYes

Fingerprint

Ebstein Anomaly
Cardiac Arrhythmias
Sudden Death
Atrioventricular Nodal Reentry Tachycardia
Mediastinitis
Wolff-Parkinson-White Syndrome
Atrial Flutter
Tricuspid Valve
Ventricular Tachycardia
Tachycardia
Atrial Fibrillation
Catheters
Morbidity
Survival
Mortality

Keywords

  • Concomitant arrhythmia ablation
  • Ebstein's anomaly
  • Electrophysiological study

ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine

Cite this

Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein's anomaly. / Huang, C. J.; Chiu, I. S.; Lin, F. Y.; Chen, W. J.; Lin, J. L.; Lo, H. M.; Wu, M. H.; Chu, S. H.

In: Thoracic and Cardiovascular Surgeon, Vol. 48, No. 6, 01.12.2000, p. 347-350.

Research output: Contribution to journalArticle

Huang, C. J. ; Chiu, I. S. ; Lin, F. Y. ; Chen, W. J. ; Lin, J. L. ; Lo, H. M. ; Wu, M. H. ; Chu, S. H. / Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein's anomaly. In: Thoracic and Cardiovascular Surgeon. 2000 ; Vol. 48, No. 6. pp. 347-350.
@article{f1dbbe35efab4dac8cbf8e1ab57c29e5,
title = "Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein's anomaly",
abstract = "Background: Repairing Ebstein's anomaly without correction of associated arrhythmia may result in sudden death. Catheter or surgical ablation is indicated for various symptomatic tachyarrhythmias in Ebstein's anomaly. Methods: Between October 1973 and October 1997, 30 patients with Ebstein's anomaly underwent surgical repair in our hospital. Tricuspid valve replacement was performed in 13 patients, tricuspid annuloplasty and valvuloplasty in the remaining 17 patients. Preoperative electrophysiological studies were performed in 11 patients after 1980. Concomitant arrhythmia ablation was done in 10 patients: 4 for Wolff-Parkinson-White syndrome, 2 for atrioventricular (AV) nodal reentrant tachycardia, one for ventricular tachycardia and 3 for paroxysmal atrial flutter and fibrillation. Results: No mortality or major morbidity occurred in those patients undergoing arrhythmia intervention. There were 7 deaths in total; 6 died suddenly, and the other died of purulent mediastinitis. None of the 6 sudden deaths underwent preoperative electrophysiological evaluation. The functional recovery was good in all survivals. Conclusions: We conclude that detailed preoperative electrophysiological evaluation in patients with Ebstein's anomaly is mandatory. Aggressive surgical intervention of the associated arrhythmias in addition to anatomic correction can reduce the sudden death in Ebstein's anomaly.",
keywords = "Concomitant arrhythmia ablation, Ebstein's anomaly, Electrophysiological study",
author = "Huang, {C. J.} and Chiu, {I. S.} and Lin, {F. Y.} and Chen, {W. J.} and Lin, {J. L.} and Lo, {H. M.} and Wu, {M. H.} and Chu, {S. H.}",
year = "2000",
month = "12",
day = "1",
doi = "10.1055/s-2000-8348",
language = "English",
volume = "48",
pages = "347--350",
journal = "Thoracic and Cardiovascular Surgeon",
issn = "0171-6425",
publisher = "Georg Thieme Verlag",
number = "6",

}

TY - JOUR

T1 - Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein's anomaly

AU - Huang, C. J.

AU - Chiu, I. S.

AU - Lin, F. Y.

AU - Chen, W. J.

AU - Lin, J. L.

AU - Lo, H. M.

AU - Wu, M. H.

AU - Chu, S. H.

PY - 2000/12/1

Y1 - 2000/12/1

N2 - Background: Repairing Ebstein's anomaly without correction of associated arrhythmia may result in sudden death. Catheter or surgical ablation is indicated for various symptomatic tachyarrhythmias in Ebstein's anomaly. Methods: Between October 1973 and October 1997, 30 patients with Ebstein's anomaly underwent surgical repair in our hospital. Tricuspid valve replacement was performed in 13 patients, tricuspid annuloplasty and valvuloplasty in the remaining 17 patients. Preoperative electrophysiological studies were performed in 11 patients after 1980. Concomitant arrhythmia ablation was done in 10 patients: 4 for Wolff-Parkinson-White syndrome, 2 for atrioventricular (AV) nodal reentrant tachycardia, one for ventricular tachycardia and 3 for paroxysmal atrial flutter and fibrillation. Results: No mortality or major morbidity occurred in those patients undergoing arrhythmia intervention. There were 7 deaths in total; 6 died suddenly, and the other died of purulent mediastinitis. None of the 6 sudden deaths underwent preoperative electrophysiological evaluation. The functional recovery was good in all survivals. Conclusions: We conclude that detailed preoperative electrophysiological evaluation in patients with Ebstein's anomaly is mandatory. Aggressive surgical intervention of the associated arrhythmias in addition to anatomic correction can reduce the sudden death in Ebstein's anomaly.

AB - Background: Repairing Ebstein's anomaly without correction of associated arrhythmia may result in sudden death. Catheter or surgical ablation is indicated for various symptomatic tachyarrhythmias in Ebstein's anomaly. Methods: Between October 1973 and October 1997, 30 patients with Ebstein's anomaly underwent surgical repair in our hospital. Tricuspid valve replacement was performed in 13 patients, tricuspid annuloplasty and valvuloplasty in the remaining 17 patients. Preoperative electrophysiological studies were performed in 11 patients after 1980. Concomitant arrhythmia ablation was done in 10 patients: 4 for Wolff-Parkinson-White syndrome, 2 for atrioventricular (AV) nodal reentrant tachycardia, one for ventricular tachycardia and 3 for paroxysmal atrial flutter and fibrillation. Results: No mortality or major morbidity occurred in those patients undergoing arrhythmia intervention. There were 7 deaths in total; 6 died suddenly, and the other died of purulent mediastinitis. None of the 6 sudden deaths underwent preoperative electrophysiological evaluation. The functional recovery was good in all survivals. Conclusions: We conclude that detailed preoperative electrophysiological evaluation in patients with Ebstein's anomaly is mandatory. Aggressive surgical intervention of the associated arrhythmias in addition to anatomic correction can reduce the sudden death in Ebstein's anomaly.

KW - Concomitant arrhythmia ablation

KW - Ebstein's anomaly

KW - Electrophysiological study

UR - http://www.scopus.com/inward/record.url?scp=0034532574&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0034532574&partnerID=8YFLogxK

U2 - 10.1055/s-2000-8348

DO - 10.1055/s-2000-8348

M3 - Article

C2 - 11145402

AN - SCOPUS:0034532574

VL - 48

SP - 347

EP - 350

JO - Thoracic and Cardiovascular Surgeon

JF - Thoracic and Cardiovascular Surgeon

SN - 0171-6425

IS - 6

ER -