Neuroradiological findings in atypical teratoid/rhabdoid tumor of the central nervous system

Y. C. Cheng, J. F. Lirng, F. C. Chang, W. Y. Guo, M. M.H. Teng, C. Y. Chang, Tai-Tong Wong, D. M.T. Ho

Research output: Contribution to journalArticle

45 Citations (Scopus)

Abstract

Purpose: To evaluate the computed tomography (CT) and magnetic resonance imaging (MRI) findings of atypical teratoid tumor/rhabdoid tumor (AT/RT) of the central nervous system (CNS). Material and methods: Twenty cases of CNS AT/RT have been found over the past 23 years in our hospital; these involving 11 boys and 9 girls whose mean age at diagnosis was 5.5 years. Their clinical data, the CT, and MRI findings were reviewed retrospectively. Results: AT/RT was located in the cerebellum in 15 cases. Four cases arose from the supratentorial region, while only one occurred primarily in the lumbar spinal cord. Almost all cases revealed heterogeneous intensity and heterogeneous enhancement. Peripheral cystic components were common. Survival time ranged from 2 months to 3 years, with a mean survival of 11.6 months. Conclusion: Most cases of AT/RT are located in the cerebellum. The radiologic manifestations are non-specific. The diagnosis mainly depends on the pathologic findings. However, AT/RT should still remain in the differential diagnosis of brain tumors in young children, especially those located in the cerebellar hemisphere and with eccentric cysts.

Original languageEnglish
Pages (from-to)89-96
Number of pages8
JournalActa Radiologica
Volume46
Issue number1
DOIs
Publication statusPublished - Feb 1 2005
Externally publishedYes

Fingerprint

Rhabdoid Tumor
Nervous System Neoplasms
Central Nervous System
Cerebellum
Spinal Cord
Tomography
Magnetic Resonance Imaging
Survival
Brain Neoplasms
Cysts
Differential Diagnosis
Typical Teratoid Rhabdoid Tumor
Atypical Teratoid Tumor

Keywords

  • Brain neoplasm
  • Computed tomography
  • Magnetic resonance imaging

ASJC Scopus subject areas

  • Radiological and Ultrasound Technology
  • Radiology Nuclear Medicine and imaging

Cite this

Cheng, Y. C., Lirng, J. F., Chang, F. C., Guo, W. Y., Teng, M. M. H., Chang, C. Y., ... Ho, D. M. T. (2005). Neuroradiological findings in atypical teratoid/rhabdoid tumor of the central nervous system. Acta Radiologica, 46(1), 89-96. https://doi.org/10.1080/02841850510020987

Neuroradiological findings in atypical teratoid/rhabdoid tumor of the central nervous system. / Cheng, Y. C.; Lirng, J. F.; Chang, F. C.; Guo, W. Y.; Teng, M. M.H.; Chang, C. Y.; Wong, Tai-Tong; Ho, D. M.T.

In: Acta Radiologica, Vol. 46, No. 1, 01.02.2005, p. 89-96.

Research output: Contribution to journalArticle

Cheng, YC, Lirng, JF, Chang, FC, Guo, WY, Teng, MMH, Chang, CY, Wong, T-T & Ho, DMT 2005, 'Neuroradiological findings in atypical teratoid/rhabdoid tumor of the central nervous system', Acta Radiologica, vol. 46, no. 1, pp. 89-96. https://doi.org/10.1080/02841850510020987
Cheng, Y. C. ; Lirng, J. F. ; Chang, F. C. ; Guo, W. Y. ; Teng, M. M.H. ; Chang, C. Y. ; Wong, Tai-Tong ; Ho, D. M.T. / Neuroradiological findings in atypical teratoid/rhabdoid tumor of the central nervous system. In: Acta Radiologica. 2005 ; Vol. 46, No. 1. pp. 89-96.
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