Nasal Rosai-Dorfman disease with intracranial involvement: A case report

Yu Chien Chang, Ming Hsui Tsai, Chi Long Chen, Chon Haw Tsai, Alex Ying Shyuan Lee

Research output: Contribution to journalArticle

13 Citations (Scopus)

Abstract

Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) is a rare but distinctive entity. It was initially described as a nodal-based disease but later found to affect a variety of extranodal sites. The diagnosis of Rosai-Dorfman disease is based on the unique histologic changes that are characterized by proliferation of S-100 protein-positive histiocytes, the presence of emperipolesis, and a mixture of prominent lymphoplasmacytic infiltrates. The etiology of Rosai-Dorfman disease is unknown. It usually runs a benign clinic course and may resolve spontaneously, but cases running protracted courses have also been reported. We report an unusual case of recurrent extranodal Rosai-Dorfman disease in nasal and paranasal cavities with intracranial involvement surviving for more than 9 years.

Original languageEnglish
Pages (from-to)183-186
Number of pages4
JournalAmerican Journal of Otolaryngology - Head and Neck Medicine and Surgery
Volume24
Issue number3
DOIs
Publication statusPublished - May 2003
Externally publishedYes

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Sinus Histiocytosis
Nose
Emperipolesis
Histiocytes
S100 Proteins
Nasal Cavity

ASJC Scopus subject areas

  • Otorhinolaryngology

Cite this

Nasal Rosai-Dorfman disease with intracranial involvement : A case report. / Chang, Yu Chien; Tsai, Ming Hsui; Chen, Chi Long; Tsai, Chon Haw; Lee, Alex Ying Shyuan.

In: American Journal of Otolaryngology - Head and Neck Medicine and Surgery, Vol. 24, No. 3, 05.2003, p. 183-186.

Research output: Contribution to journalArticle

Chang, Yu Chien ; Tsai, Ming Hsui ; Chen, Chi Long ; Tsai, Chon Haw ; Lee, Alex Ying Shyuan. / Nasal Rosai-Dorfman disease with intracranial involvement : A case report. In: American Journal of Otolaryngology - Head and Neck Medicine and Surgery. 2003 ; Vol. 24, No. 3. pp. 183-186.
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