Multicystic dysplastic kidney disease presenting with a single large cyst in a fetus-anatomical basis and radiological aspects

Fong Fong Lim, Teng Fu Tsao, Hung Ming Chang, Ji Nan Sheu

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5 Citations (Scopus)


Multicystic dysplastic kidney (MCDK) is a congenital maldevelopment in which the renal cortex is characteristically replaced by numerous cysts of multiple sizes. MCDK presenting as a single predominant large cyst in morphology is less common. We report on the prenatal imaging findings and perinatal management of a fetus with MCDK unusually presenting as a single predominant large cyst, erroneously interpreted as a severe fetal hydronephrosis. Details of the perinatal history, radiological evaluation, morphological characteristic, and clinical aspect of this case are presented. We also discuss a few studies addressing the sensitivity of magnetic resonance urography for the prenatal diagnosis of MCDK.

Original languageEnglish
Pages (from-to)227-231
Number of pages5
JournalPediatrics and Neonatology
Issue number4
Publication statusPublished - Aug 2011
Externally publishedYes



  • fetal hydronephrosis
  • fetal magnetic resonance imaging
  • multicystic dysplastic kidney
  • single predominant large cyst

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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