Multicentric reticulohistiocytosis in a Taiwanese woman with Sjögren syndrome

Lan hsin Cheng, Ying Yi Chiang

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1 Citation (Scopus)

Abstract

Multicentric reticulohistiocytosis is a rare, non-Langerhans cell histiocytosis characterized by specific skin lesions and destructive arthritis. Clinically, it generally presents with multiple reddish-brown papulonodules over the hands, face, and trunk. The associated destructive arthropathy tends to be severe, with 50% of patients developing arthritis mutilans. Approximately 25-30% of patients present with neoplasia. Coexisting autoimmune diseases are also commonly reported. Here we report the case of a 59-year-old Taiwanese woman with underlying Sjögren syndrome who presented with the typical skin manifestations of multicentric reticulohistiocytosis and early interphalangeal joint involvement. The patient later showed partial response to methotrexate treatment.

Original languageEnglish
Pages (from-to)42-45
JournalDermatologica Sinica
Volume34
Issue number1
DOIs
Publication statusPublished - Mar 1 2016

Keywords

  • Dermatomyositis
  • Erosive polyarthropathy
  • Multicentric reticulohistiocytosis
  • Non-langerhans cell histiocytosis
  • Sjögren syndrome

ASJC Scopus subject areas

  • Dermatology

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