Linear Scleroderma "En Coup De Sabre": Initial Presentation as Intractable Partial Seizures in a Child

Kuo Liang Chiang, Kai Ping Chang, Tai-Tong Wong, Ting Rong Hsu

Research output: Contribution to journalArticle

21 Citations (Scopus)

Abstract

Linear scleroderma is a form of localized scleroderma characterized by sclerotic lesions distributed in a linear, band-like pattern. The "en coup de sabre" subtype of linear scleroderma is more often associated with systemic morbidity, including ocular, oral, and neurological abnormalities. Here, we report one patient with typical linear scleroderma "en coup de sabre" (LSCS). Initially, he presented with refractory partial seizures before the characteristic skins lesion on his head developed. This was a rare case with obvious brain parenchyma involvement. We did not prescribe medication but performed serial brain magnetic resonance imaging follow-up for the intraparenchymal lesion. The atrophic changes of the skin, face and brain remained the same, and his seizures had not worsened at the most recent follow-up. Parry-Romberg syndrome, a very similar condition, should be differentiated from LSCS.

Original languageEnglish
Pages (from-to)294-298
Number of pages5
JournalPediatrics and Neonatology
Volume50
Issue number6
DOIs
Publication statusPublished - Dec 1 2009
Externally publishedYes

Keywords

  • intractable seizure
  • linear scleroderma en coup de sabre
  • progressive brain atrophy

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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