A Case of Behçet’s Disease with Pulmonary Artery Aneurysm and Deep Venous Thrombosis

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Abstract

Introduction: Behçet’s disease is a multisystemic disorder characterized by recurrent orogenital ulcers, ocular manifestations, and skin lesions. It is more prevalent in men of young age. Here we describe a patient with Behçet’s disease of cardiovascular and chest symptoms.
Case Report: A 22-year-old man presented with recurrent abdominal fullness, left flank pain and dysuria and came to our hospital. Chest computed tomography showed severe thrombosis involving the inferior vena cava, bilateral iliac, left renal veins and also the pulmonary artery with aneurysm formation. He underwent inferior vena caval thrombectomy and filtering, and started oral anticoagulant therapy. However, intermittent hemoptysis drove him to the hospital again after six months. The persistence of pulmonary arterial thrombosis and development of pulmonary hemorrhage were noted. Further examinations revealed that he had Behçet’s disease.
Discussion: Behçet’s disease primarily involves four main systems: the cardiovascular, chest, gastrointestinal and central nervous systems. Complications in the cardiovascular system may affect arteries and veins of differing sizes in various organs. Inflammation of the arteries can lead to wall thickening and aneurysm formation, whereas inflammation of the veins results in thrombosis. Chest manifestations affect about 1-8% of patients, which represent multiple and bilateral pulmonary arteritis and thrombosis resulting in infarction, hemorrhage, and focal atelectasis. Differential diagnosis of pulmonary arteritis in young patients includes ANCA-associated vasculitides and Takayasu’s arteritis. Behçet’s disease may resolve with corticosteroids, immunosuppressants and colchicine. Anticoagulant therapy and surgery are not recommended for risk of complications and recurrence.
Translated title of the contribution一貝歇氏症候群案例併肺動脈瘤及深部靜脈栓塞
Original languageEnglish
Title of host publicationRSROC2018中華民國放射線醫學會
Publication statusPublished - 2018

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